Panel 22 · Endocrine & Metabolic Endocrinology

Disorders/Differences of Sex Development Panel

Differences of sex development and gonadal determination disorders.

Panel number
22 of 58
Clinical category
Endocrine & Metabolic Endocrinology
Genes on this panel
275
Original panel title
Cinsiyet Gelişim Paneli
Source version
PANEL LİSTESİ V9
Requested via
Rare Disease Genomics

Gene content

275 genes

All 275 gene symbols in source order
  • ABCD1
  • AIP
  • AIRE
  • AKR1C2
  • AKR1C4
  • AKT1
  • ALDOA
  • ALG1
  • ALMS1
  • AMACR
  • AMH
  • AMHR2
  • ANOS1
  • ANTXR1
  • AR
  • ARL2BP
  • ARL6
  • ARX
  • ATAD3A
  • ATPAF2
  • ATM
  • ATRX
  • BAZ1B
  • BBS1
  • BBS10
  • BBS12
  • BBS2
  • BBS4
  • BBS5
  • BBS7
  • BCS1L
  • BCOR
  • BMPR1B
  • BMP15
  • BMP2
  • BMP4
  • BRCA2
  • BRCC3
  • BTK
  • CA4
  • CAMKMT
  • CASK
  • CBL
  • CBX2
  • CCDC28B
  • CCNQ
  • CDH23
  • CDKN1C
  • CEP41
  • CHD7
  • CHRNG
  • CISD2
  • CLIP2
  • CLPP
  • CNBP
  • COQ2
  • CPE
  • CREBBP
  • CTDP1
  • CTNS
  • CUL4B
  • CUL7
  • CYB5A
  • CYP11A1
  • CYP11B1
  • CYP17A1
  • CYP19A1
  • CYP21A2
  • DCAF17
  • DHDDS
  • DHH
  • DHCR7
  • DHX37
  • DMRT1
  • DYNC2H1
  • EIF2B1
  • EIF2S3
  • EIF4H
  • EMX2
  • ERCC2
  • ERCC3
  • ESR2
  • ESCO2
  • FANCA
  • FANCB
  • FANCC
  • FANCD2
  • FANCE
  • FANCF
  • FANCL
  • FANCM
  • FAT4
  • FGD1
  • FGF8
  • FGFR1
  • FGFRL1
  • FIG4
  • FIGLA
  • FKBP6
  • FOXA2
  • FOXL2
  • FRAS1
  • FREM2
  • FSHB
  • FSHR
  • GATA4
  • GHR
  • GHSR
  • GLI2
  • GLI3
  • GNAS
  • GNRH1
  • GNRHR
  • GRB10
  • GRIA1
  • GRIP1
  • GRM7
  • GTF2I
  • GTF2IRD1
  • H6PD
  • HCCS
  • HESX1
  • HFE
  • HOXA13
  • HSD17B3
  • HSD3B2
  • ICK
  • IER3IP1
  • IFT27
  • IFT88
  • IFT172
  • IGF1
  • INSR
  • IRF6
  • KLHL7
  • KISS1
  • KISS1R
  • KMT2D
  • KRAS
  • LEP
  • LEPR
  • LHB
  • LHCGR
  • LHX3
  • LHX4
  • LIG3
  • LIMK1
  • LMNA
  • LZTR1
  • MAGEL2
  • MAMLD1
  • MAP3K1
  • MECP2
  • MEN1
  • MKKS
  • MKS1
  • MLXIP
  • NDN
  • NEK1
  • NF1
  • NIPBL
  • NOTCH2
  • NPHP1
  • NR0B1
  • NR2F2
  • NR3C1
  • NR5A1
  • NRAS
  • NSMF
  • OCRL
  • OFD1
  • OPA1
  • OTX2
  • PALB2
  • PAPSS2
  • PBX1
  • PCSK1
  • PDE11A
  • PDE4D
  • PEX1
  • PEX6
  • PGM1
  • PHF6
  • PHGDH
  • PIGA
  • PMM2
  • PNPLA6
  • POLD1
  • POLG
  • POLR1C
  • POLR3A
  • POLR3B
  • POR
  • POU1F1
  • PPM1B
  • PRKAR1A
  • PRLR
  • PROK2
  • PROKR2
  • PROP1
  • PSMC3IP
  • PTCH1
  • PTPN11
  • RAB18
  • RAB23
  • RAB3GAP1
  • RAB3GAP2
  • RAD51
  • RAD51C
  • RAF1
  • RBM28
  • RECQL4
  • RERE
  • RHO
  • RIN2
  • RIPK4
  • RIT1
  • ROBO1
  • ROR2
  • RRAS2
  • RSPO1
  • SALL1
  • SAMD9
  • SDCCAG8
  • SEMA3A
  • SEMA3E
  • SHH
  • SIL1
  • SIM1
  • SIX3
  • SKI
  • SLC29A3
  • SMAD4
  • SMARCE1
  • SMCHD1
  • SMO
  • SNAP29
  • SOS1
  • SOS2
  • SOX10
  • SOX2
  • SOX3
  • SOX9
  • SPECC1L
  • SPRY4
  • SRCAP
  • SRD5A2
  • SRY
  • STAR
  • STAT1
  • STAT3
  • STAT5B
  • STK11
  • STS
  • TBX15
  • TBX3
  • TFR2
  • TOE1
  • TP53
  • TP63
  • TSC1
  • TSC2
  • TSPYL1
  • TTC8
  • TWIST2
  • UBR1
  • WDR11
  • WFS1
  • WNT4
  • WNT7A
  • WRN
  • WT1
  • ZBTB20
  • ZFPM2
  • ZMPSTE24

Gene symbols are reproduced from the department’s current NGS panel source document (PANEL LİSTESİ V9), in source order. No symbol has been added, removed, renamed or expanded, and none has been reconciled against an earlier edition of the catalogue or against an external gene database. Panel titles, gene counts and gene content are published as confirmed by the department. Panel composition may be revised; the version in force at the time of testing applies.