Panel 54 · Skeletal & Connective Tissue

Osteogenesis Imperfecta Panel

Osteogenesis imperfecta and other inherited disorders of bone fragility.

Panel number
54 of 58
Clinical category
Skeletal & Connective Tissue
Genes on this panel
165
Original panel title
Osteogenezis İmperfekta Paneli
Source version
PANEL LİSTESİ V9
Requested via
Rare Disease Genomics

Gene content

165 genes

All 165 gene symbols in source order
  • ACAN
  • ACP5
  • ALPL
  • ANKH
  • ANO5
  • ATP6V0A2
  • ATRX
  • B3GALT6
  • B3GAT3
  • B4GALT7
  • BMP1
  • BMPR1B
  • CANT1
  • CASR
  • CDKN1C
  • CHST14
  • CHST3
  • CLCN5
  • COL10A1
  • COL11A1
  • COL11A2
  • COL1A1
  • COL1A2
  • COL2A1
  • COL5A1
  • COL9A1
  • COL9A2
  • COL9A3
  • COMP
  • CREBBP
  • CRTAP
  • CTSK
  • CUL7
  • CYP26B1
  • DDR2
  • DHCR24
  • DHCR7
  • DMP1
  • DSPP
  • DYM
  • DYNC2H1
  • EIF2AK3
  • ENPP1
  • EP300
  • ERCC6
  • ERCC8
  • ESR1
  • EVC
  • EVC2
  • EXT2
  • FAM20C
  • FBN1
  • FGD1
  • FGF23
  • FGFR1
  • FGFR2
  • FGFR3
  • FKBP10
  • FLNA
  • FLNB
  • GDF5
  • GH1
  • GHR
  • GHRHR
  • GHSR
  • GLI2
  • GLI3
  • GNAS
  • GNPTAB
  • GORAB
  • GPC6
  • GSC
  • HESX1
  • HSPG2
  • ICK
  • IFITM5
  • IFT122
  • IFT140
  • IFT80
  • IGF1
  • IGF1R
  • IHH
  • KDM6A
  • KIF22
  • KMT2D
  • KRAS
  • LHX3
  • LIFR
  • LMNA
  • LRP4
  • LRP5
  • LRP6
  • MAFB
  • MATN3
  • MBTPS2
  • MESD
  • MMP13
  • MMP2
  • MMP9
  • NBAS
  • NEK1
  • NIPBL
  • NKX3-2
  • NOTCH2
  • NPR2
  • OBSL1
  • OFD1
  • P3H1
  • PAPSS2
  • PCNT
  • PHEX
  • PLOD1
  • PLOD2
  • POC1A
  • POU1F1
  • PPIB
  • PRKAR1A
  • PROP1
  • PTH1R
  • PTPN11
  • PTPRQ
  • PYCR1
  • RAF1
  • ROR2
  • RPS6KA3
  • RUNX2
  • SERPINF1
  • SERPINH1
  • SH3PXD2B
  • SHOX
  • SHOX2
  • SLC26A2
  • SLC34A3
  • SLC35D1
  • SLC39A13
  • SMC1A
  • SMC3
  • SOS1
  • SOST
  • SOX2
  • SOX3
  • SOX9
  • SP7
  • SRCAP
  • STAT5B
  • SUCO
  • TBCE
  • TCTN3
  • THRB
  • TMCO1
  • TNFRSF11A
  • TNXB
  • TREM2
  • TRIM37
  • TRIP11
  • TRPS1
  • TRPV4
  • TRPV6
  • TYROBP
  • VDR
  • WDR35
  • WNT1
  • WNT5A
  • WRN
  • ZMPSTE24

Gene symbols are reproduced from the department’s current NGS panel source document (PANEL LİSTESİ V9), in source order. No symbol has been added, removed, renamed or expanded, and none has been reconciled against an earlier edition of the catalogue or against an external gene database. Panel titles, gene counts and gene content are published as confirmed by the department. Panel composition may be revised; the version in force at the time of testing applies.